Particularities and Surgical Treatment of Constriction Band Syndrome Syndactyly, in Children


Constriction band syndrom syndactyly is a sporadic condition, that may be present in association with other congenital anomalies such as musculoskeletal (including total amputation of the limb), craniofacial (like cleft lip and cleft palate) and thoraco-abdominal disorders (such as gastroschisis and extrathoracic heart), neural tube defects, scoliosis and hemangiomas (1, 2, 3, 4, 5, 6). Some of these manifestations are uncommonly noted at birth because they result in spontaneous abortion.
There are two main theories about constriction band syndrome etiology, the first of which is the intrinsic theory proposed by George Streeter, the director of embryology at Carnegie Institute, in 1930 which is called, “Streeter¬ís Dysplasia”. Streeter suggested that an intrinsic defect in the subcutaneous germplasm resulted in focal mesenchymal hypoplasia, tissue loss, and scarring (7, 8).