Aggressive Nasal Type Extranodal Natural killer/T-cell Lymphoma Presenting as Refractory Granulomatosis with Polyangiitis…

We present a rare case of nasal type extranodal NK/T-cell lymphoma mimicking granulomatosis with polyangiitis (GPA), in order to highlight the difficulties in the differential diagnosis of destructing nasal lesions. Extranodal NK/T-cell lymphoma, nasal type is a rare type of non-Hodgkin’s lymphoma, often associated with Epstein-Barr virus (EBV) infection, characterised by destructive lesions arising in the naso-sinusal tract and progressively invading the midfacial bones. […]