The purpose of our paper is to study the results of surgical treatment of patients with congenital high standing of the scapula. Congenital high standing of the scapula, Sprengel disease is a complex combination of anomalies in the development of the shoulder girdle, spine and chest. The main clinical manifestations of the pathology are the high standing of the shoulder blade of the abduction restriction in the shoulder joint and a pronounced cosmetic defect. The results of surgical treatment of patients with congenital high standing of the scapula, taking into account the form and severity of the disease were studied. The study was conducted at the Department of Pediatric Orthopedics of RSSPMCTO. 85 children aged 3 to 14 years with congenital high standing of the scapula were treated for the period from 2005 to 2018, there were 26 (31%) boys and girls – 59 (69%). Patients with congenital high position of the scapula underwent Ternovsky 11 (13%) and Pozdeev 74 (87%) surgery. After the operation, the thoracobrachial cast were put on patients for 4 weeks. In addition, it was prescribed the physiotherapy exercises on the ﬁngers and UHF on top of the plaster cast. Long-term results showed that out of 85 (100%) patients 73 (86%) were good and 12 (14%) were satisfactory. Evaluation of treatment results was carried out according to cosmetic and functional parameters. Our research conclusions show that the operation according to the Pozdeev method is atraumatic and it is the method of choice for surgical treatment of Sprengel disease in children.